バルーン肺動脈形成術後にガイドワイヤーが抜去できず断裂したWilliams症候群の小児例Guidewire entrapment and fracture during balloon pulmonary angioplasty in a pediatric case with Williams syndrome
兵庫県立こども病院 循環器内科Department of Cardiology, Kobe Children’s Hospital, Hyogo, Japan
兵庫県立こども病院 循環器内科Department of Cardiology, Kobe Children’s Hospital, Hyogo, Japan
症例はWilliams症候群,大動脈弁上狭窄,末梢性肺動脈狭窄の11か月女児.大動脈弁上拡大術,冠動脈入口部形成術,肺動脈形成術を施行したが,右室圧高値のため体外式膜型人工肺下で手術を終了した.術後8日目バルーン肺動脈形成術(Balloon pulmonary angioplasty; 以下BPA)を行った.左右肺動脈5病変に対してBPAを行った.いずれも0.014インチAguru™ガイドワイヤー,3 mmバルーンを用いた.6病変目としての右上肺動脈の径1 mmのびまん性狭窄に対して同システムでBPAを行った.施行後ガイドワイヤーが抜去できず,引き抜くとアンラベルした.ピッグテイル,スネアカテーテルを用いたが,アンラベル箇所が切断された.外科的抜去を施行したが全抜去は困難であった.肺動脈のびまん性狭窄病変ではガイドワイヤーの抜去困難が起こりうる.金属疲労のあるガイドワイヤーは断裂の可能性を念頭に置く.
The case involved an 11-month-old female infant with Williams syndrome, supravalvular aortic stenosis, and peripheral pulmonary artery stenosis. She underwent supravalvular aortic enlargement, coronary ostial plasty, and pulmonary arterioplasty. Due to elevated right ventricular pressure, the surgery was completed under extracorporeal membrane oxygenation. Balloon pulmonary angioplasty (BPA) was performed on the 8th day postoperatively for both pulmonary arteries. BPA was performed on five lesions in the left and right pulmonary artery, using a 0.014-inch Aguru™ guidewire and a 3 mm balloon. As the sixth procedure, BPA was performed for diffuse stenotic lesion of the right upper pulmonary artery with a 1 mm diameter using the same guidewire and balloon. After BPA, the guidewire became irretrievable. Attempts to retrieve the guidewire with a pigtail catheter and a snare catheter were unsuccessful. Surgical removal was attempted, but removal was not possible completely. Guidewire entrapment can occur in cases of diffuse stenotic lesions in pulmonary arteries. We need to consider the risk of fracture in guidewires with metal fatigue.
Key words: guidewire; entrapment; fracture; pulmonary artery; Williams syndrome
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